Subject(s)
Humans , Male , Middle Aged , Fibromatosis, Abdominal/pathology , Intestinal Obstruction/etiology , Mesentery/pathology , Peritoneal Neoplasms/pathology , Colectomy/methods , Diagnosis, Differential , Duodenum/surgery , Fibromatosis, Abdominal/complications , Fibromatosis, Abdominal/surgery , Intestinal Obstruction/diagnosis , Jejunum/surgeryABSTRACT
El Tumor Desmolde o Fibromatosis Mesentérica es una enfermedad infrecuente en la que se reconocen 2 formas: una esporádica y otra asociada a poliposis familiar adenomatosa. De etiología desconocida, su diagnóstico preoperatorio es dificultoso y el tratamiento de elección es quirúrgico. Se pone en consideración un caso de esta entidad en un varón joven, que se presentó con dolor abdominal y fiebre. Se realizó cirugía resectiva agresiva, otorgándose el alta a los 18 días de la intervención.
Desmoid tumor or mesenteric fibromatosis is an uncommon disease with to variants: a sporadic form and one associated to familial adenomatous polyposis. Surgery is the treatment of choice. We report a 45 years old male presenting with abdominal pain and fever. An abdominal ultrasound informed the presence of a mass in the periumblical area. An Abdominal CAT sean showed a 13 cm diameter solid mass located in the left upper quadrant. The patient was operated and that mass is excised, requiring also a hemicolectomy, excision of the fourth portion of the duodenum and cholecystectomy. The pathology report of the excised tumor informs a mesenteric fibromatosis. The patient was discharged at the 18th postoperative day.
Subject(s)
Humans , Male , Middle Aged , Fibromatosis, Abdominal/surgery , Fibromatosis, Abdominal/complications , Mesentery , Peritoneal Neoplasms/surgery , Abdominal Pain/etiology , Fibroma , Treatment OutcomeABSTRACT
Primary mesenteric fibromatosis is a rare condition. The aggressive nature of these tumors and the potential for major morbidity secondary to resection makes it a challenging disease for the surgeon. We report a case of mesenteric fibromatosis with involvement of small bowel.